Genomic aberrations of the CACNA2D1 gene in three patients with epilepsy and intellectual disability.

Center for Medical Genetics, Ghent University, Ghent University Hospital, Ghent, Belgium. Laboratory for Clinical and Experimental Neurophysiology, Neurobiology and Neuropsychology, Department of Neurology, Ghent University, Ghent University Hospital, Ghent, Belgium. Centrum voor Ontwikkelingsstoornissen (COS), Ghent University Hospital, Ghent, Belgium. Service de Génétique Médicale, Institut de Biologie, Nantes, France. Service de Pédiatrie, CHU, Nantes, France.

European journal of human genetics : EJHG. 2015;(5):628-32

Abstract

Voltage-gated calcium channels have an important role in neurotransmission. Aberrations affecting genes encoding the alpha subunit of these channels have been associated with epilepsy and neuropsychiatric disorders such as autism or schizophrenia. Here we report three patients with a genomic aberration affecting the CACNA2D1 gene encoding the α2δ subunit of these voltage-gated calcium channels. All three patients present with epilepsy and intellectual disability pinpointing the CACNA2D1 gene as an interesting candidate gene for these clinical features. Besides these characteristics, patient 2 also presents with obesity with hyperinsulinism, which is very likely to be caused by deletion of the CD36 gene.

Methodological quality

Publication Type : Case Reports

Metadata

MeSH terms : Calcium Channels